Genetic Information

Gene & Transcript Details

Gene
PIK3CA
Transcript
NM_006218.4 MANE Select
Total Exons
Reference Sequence
NC_000003.11
Alternative Transcripts
IDStatusDetails
NM_006218.2 Alternative 3724 nt | 158–3364
NM_006218.3 Alternative 9104 nt | 158–3364
NM_006218.4 MANE Select 9259 nt | 324–3530

Variant Details

HGVS Notation
NM_006218.4:c.1813A>G
Protein Change
N605D
Location
Exon 12 (Exon 12 of )
12
5'Exon Structure3'
Functional Consequence
Loss of Function
Alternate Identifiers

Clinical & Population Data

Population Frequency

gnomAD
Global Frequency
0.0 in 100,000
Extremely Rare
ACMG Criteria Applied PM2
This variant is absent or extremely rare in population databases (PM2 criteria applies).

ClinVar

Open
Classification
Unknown
0 publications
Clinical Statement

""

COSMIC Somatic Evidence

Open
COSMIC ID
Recurrence
0 occurrences
PM1 Criteria
Not Applied
COSMIC Database Preview
COSMIC Preview
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Functional Impact & Domains

Functional Domain

Hotspot Status
Not a hotspot
Domain Summary
This variant is not located in a mutational hotspot or critical domain.
Related Variants in This Domain
No evidence of other pathogenic variants at this position in gene PIK3CA.

Functional Studies & Therapeutic Relevance

Functional Summary

The PIK3CA N605D variant has not been functionally characterized.

Database Previews
OncoKB
OncoKB Preview
JAX-CKB
JAX-CKB Preview

Click on previews to view full database entries. External databases may require institutional access.

Computational Analysis

Pathogenicity Predictions

SpliceAI
Predictor Consensus
Mixed/VUS
PP3 Applied
No
REVEL Score
0.21
Threshold: ≥0.75 = PP3 applied

SpliceAI Scores

Window: ±500bp
Effect Type Score Position
- Acceptor Loss (AL) 0.0 263 bp
- Donor Loss (DL) 0.03 -3 bp
+ Acceptor Gain (AG) 0.01 -21 bp
+ Donor Gain (DG) 0.01 24 bp
High impact (≥0.5) Medium impact (0.2-0.49) Low impact (<0.2)

VCEP Guidelines

Applied ACMG/AMP Criteria (VCEP Specific)

Filter Criteria:
PVS1

PVS1 (Not Applied)

According to standard ACMG guidelines, PVS1 is a null variant in a gene where loss of function is a known disease mechanism. The evidence for this variant shows it is a missense change (N605D), not a null variant. Therefore, this criterion is not applied.

PS1

PS1 (Not Applied)

According to standard ACMG guidelines, PS1 is the same amino acid change as a previously established pathogenic variant regardless of nucleotide change. The evidence for this variant shows no known pathogenic N605D at this residue. Therefore, this criterion is not applied.

PS2

PS2 (Not Applied)

According to VCEP guidelines, PS2 requires confirmed de novo occurrence with parental and tissue evidence. The evidence for this variant shows no de novo or parental data. Therefore, this criterion is not applied.

PS3

PS3 (Not Applied)

According to VCEP guidelines, PS3 requires well-validated functional studies demonstrating a damaging effect. The evidence for this variant shows no functional data. Therefore, this criterion is not applied.

PS4

PS4 (Not Applied)

According to VCEP guidelines, PS4 is based on case counts and phenotype points for variants absent from controls. The evidence for this variant shows no reported cases or phenotype data. Therefore, this criterion is not applied.

PM1

PM1 (Not Applied)

According to VCEP guidelines, PM1_Supporting applies to residues affecting critical functional domains per Table 4. The evidence for this variant shows N605 is not in a defined hotspot or critical domain. Therefore, this criterion is not applied.

PM2

PM2 (Supporting)

According to VCEP guidelines, PM2_Supporting is applied for absent or rare variants from controls in ethnically matched populations. The evidence for this variant shows it is absent from gnomAD. Therefore, this criterion is applied at Supporting strength.

PM3

PM3 (Not Applied)

According to standard ACMG guidelines, PM3 applies to recessive disorders with observed trans occurrences. The evidence for this variant shows no recessive context or trans observations. Therefore, this criterion is not applied.

PM4

PM4 (Not Applied)

According to standard ACMG guidelines, PM4 applies to protein length changes. The evidence for this variant shows a single amino acid substitution without length change. Therefore, this criterion is not applied.

PM5

PM5 (Not Applied)

According to VCEP guidelines, PM5_Moderate applies for novel missense changes at residues with known pathogenic missense changes. The evidence for this variant shows no other pathogenic variants at residue N605. Therefore, this criterion is not applied.

PM6

PM6 (Not Applied)

According to standard ACMG guidelines, PM6 applies to assumed de novo variants without confirmation. The evidence for this variant shows no de novo data. Therefore, this criterion is not applied.

PP1

PP1 (Not Applied)

According to standard ACMG guidelines, PP1 supports segregation in affected family members. The evidence for this variant shows no segregation data. Therefore, this criterion is not applied.

PP2

PP2 (Not Applied)

According to VCEP guidelines, PP2_Supporting applies if ExAC/gnomAD missense constraint z-score >3.09. The evidence for this variant shows no z-score data provided. Therefore, this criterion is not applied.

PP3

PP3 (Not Applied)

According to standard ACMG guidelines, PP3 requires multiple computational predictions supporting a deleterious effect. The evidence for this variant shows predominantly benign in silico predictions. Therefore, this criterion is not applied.

PP4

PP4 (Not Applied)

According to standard ACMG guidelines, PP4 applies to patient phenotype highly specific to a gene. The evidence for this variant shows no phenotype data. Therefore, this criterion is not applied.

PP5

PP5 (Not Applied)

According to standard ACMG guidelines, PP5 applies to reputable source classifications. The evidence for this variant shows no ClinVar or expert classification. Therefore, this criterion is not applied.

BA1

BA1 (Not Applied)

According to VCEP guidelines, BA1 applies for allele frequency >0.0926%. The evidence for this variant shows 0% frequency. Therefore, this criterion is not applied.

BS1

BS1 (Not Applied)

According to VCEP guidelines, BS1 applies for allele frequency >0.0185%. The evidence for this variant shows 0% frequency. Therefore, this criterion is not applied.

BS2

BS2 (Not Applied)

According to VCEP guidelines, BS2 requires ≥3 well-phenotyped heterozygotes or homozygotes in controls. The evidence for this variant shows none. Therefore, this criterion is not applied.

BS3

BS3 (Not Applied)

According to VCEP guidelines, BS3 requires well-validated functional studies showing no damaging effect. The evidence for this variant shows no such functional data. Therefore, this criterion is not applied.

BS4

BS4 (Not Applied)

According to VCEP guidelines, BS4 applies for lack of segregation in affected members. The evidence for this variant shows no segregation information. Therefore, this criterion is not applied.

BP1

BP1 (Not Applied)

According to standard ACMG guidelines, BP1 applies to missense variants in genes where only truncating pathogenic variants are known. The evidence for this variant shows PIK3CA pathogenicity is gain-of-function, not truncation. Therefore, this criterion is not applied.

BP2

BP2 (Not Applied)

According to standard ACMG guidelines, BP2 applies when variant is observed in cis/trans with a pathogenic variant. The evidence for this variant shows no such observations. Therefore, this criterion is not applied.

BP3

BP3 (Not Applied)

According to standard ACMG guidelines, BP3 applies to in-frame indels in repetitive regions. The evidence for this variant shows a missense SNP. Therefore, this criterion is not applied.

BP4

BP4 (Not Applied)

According to VCEP guidelines, BP4 only applies to synonymous or intronic variants when splicing tools show no impact. The evidence for this variant shows a missense change. Therefore, this criterion is not applied.

BP5

BP5 (Not Applied)

According to standard ACMG guidelines, BP5 applies when variant occurs in a case with an alternate molecular basis. The evidence for this variant shows no such context. Therefore, this criterion is not applied.

BP6

BP6 (Not Applied)

According to standard ACMG guidelines, BP6 applies to assertions from reputable sources without evidence. The evidence for this variant shows no such assertions. Therefore, this criterion is not applied.

BP7

BP7 (Not Applied)

According to VCEP guidelines, BP7 applies only to synonymous or intronic variants with low conservation. The evidence for this variant shows a missense change. Therefore, this criterion is not applied.